Tehran University of Medical Sciences Basic & Clinical Cancer Research 2228-6527 14 1 2023 02 14 37 43 Dr. Kiran Bhaisare Vilasrao Deshmukh Government Medical college , Latur Dr. Jessica Tellis Vilasrao Deshmukh Government Medical college , Latur Dr. Pramod Toshniwal Vilasrao Deshmukh Government Medical college , Latur 2022 10 13 2023 01 08 Askin tumour is an uncommon form of malignant neoplasm that develops from the soft tissues of the thoracopulmonary wall and has neuroectodermal origin and possessing an aggressive behavior.  As it mimics other common pediatric disorders such as empyema, tuberculosis, lymphoma, rhabdomyosarcoma and neuroblastoma, it acts as a great diagnostic and therapeutic challenge to the treating clinicians. Its rarity, however, contributes greatly to the absence of standardized treatment protocols further facilitating detrimental prognosis.  So, the major deciding factor of its survival rate is early and precise diagnosis followed by its treatment. The present study reports a case Askin’s tumor of child which is locally aggressive and quite rare. While making the definitive diagnosis of an Askin’s tumour of thorcopulmonary region the possibility of occurrence of other primitive neuroectodermal tumors (PNET) was not ruled out. https://bccr.tums.ac.ir/index.php/bccrj/article/view/451